Powder: -20°C for 3 years | In solvent: -80°C for 1 year
2-Hydroxy-3-methylbutanoic acid ((±)-2-Hydroxyisopentanoic Acid) is a metabolite found in the urine of patients with phenylketonuria, methylmalonic acidemia, propionic acidemia, 3-ketothiolase deficiency, isovaleric acidemia, 3-methylcrotonylglycemia, 3-hydroxy-3-methylglutaric acidemia, multiple carboxylase deficiency, glutaric aciduria, ornithine transcarbamylase deficiency, glyceroluria, tyrosinemia type I, galactosemia, and maple syrup urine disease.
説明 | 2-Hydroxy-3-methylbutanoic acid ((±)-2-Hydroxyisopentanoic Acid) is a metabolite found in the urine of patients with phenylketonuria, methylmalonic acidemia, propionic acidemia, 3-ketothiolase deficiency, isovaleric acidemia, 3-methylcrotonylglycemia, 3-hydroxy-3-methylglutaric acidemia, multiple carboxylase deficiency, glutaric aciduria, ornithine transcarbamylase deficiency, glyceroluria, tyrosinemia type I, galactosemia, and maple syrup urine disease. |
別名 | 2-Hydroxy-3-methylbutyric acid, 2-Hydroxyisovaleric Acid, (±)-2-Hydroxyisopentanoic Acid |
分子量 | 118.13 |
分子式 | C5H10O3 |
CAS No. | 4026-18-0 |
Powder: -20°C for 3 years | In solvent: -80°C for 1 year
DMSO: 55 mg/mL (465.59 mM)
You can also refer to dose conversion for different animals. 詳細
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2-Hydroxy-3-methylbutanoic acid 4026-18-0 Metabolism Others Endogenous Metabolite Inhibitor inhibit 2-Hydroxy-3-methylbutyric acid 2-Hydroxyisovaleric Acid 2 Hydroxy 3 methylbutanoic acid 2-Hydroxyisopentanoic Acid 2Hydroxy3methylbutanoic acid (±)-2-Hydroxyisopentanoic Acid inhibitor